Under the ISSVA-2025 scheme the term lymphatic malformation denotes the common cystic lesion alone, and the complex anomalies are named separately. The catalogued variants map across the five subsets below.
The common cystic lesion, macrocystic or microcystic, the isolated form of the disease.
A multifocal malformation involving several regions or organs at once.
An aggressive lymphatic anomaly with kaposiform spindle-cell foci and a consumptive coagulopathy.
Progressive osteolysis, the vanishing-bone disease, with lymphatic overgrowth into bone.
A malformation of the central conducting channels, the thoracic duct and cisterna chyli.